Síndrome de Beckwith-Wiedemann y Características Dentales: Reporte de Caso
DOI:
https://doi.org/10.21270/archi.v11i5.5606Palabras clave:
Síndrome de Beckwith-Wiedmann, Macroglossia, GenesResumen
El Síndrome de Beckwith-Wiedemann (BWS) se caracteriza por un trastorno en el cromosoma 11p15, cuyos loci tienen genes reguladores del crecimiento. Entre las numerosas características clínicas, como los defectos de la pared abdominal anterior, el onfalocele y las anomalías genitales, la más prevalente es la macroglosia, que puede provocar alteraciones en el crecimiento craneofacial. Este informe trae un caso de un niño de 9 años con el síndrome tratado en la Facultad de Odontología de la Universidad del Estado de Paraná Occidental, Brasil. Se sugirió que las anomalías dentales observadas, junto con las características comunes descritas en la literatura, pueden ser parte del amplio espectro del síndrome.
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